1. These syndromes include Muir-Torre syndrome, associated with cystic sebaceomas, Cowden syndrome, associated with multiple tricholemmomas, Carney complex associated with multiple superficial angiomyxomas, Birt-Hogg-Dubé syndrome associated with multiple fibrofolliculomas, tuberous sclerosis associated with multiple facial angiofibromas and so-called Koenen tumors, patients with renal cell cancer associated with pilar leiomyomatosis and uterine leiomyomas, Gardner syndrome associated with Gardner fibromas and nevoid basal cell carcinoma associated with multiple basal cell carcinomas in young patients.

Weitere Kombinationen stellen multiple Angiofibrome und sog. Koenen-Tumoren bei der tuberösen Sklerose, multiple kutane Leiomyome und uterine Leiomyome mit Nierenzellkarzinomen, das Gardner-Fibrom mit dem Gardner-Syndrom und multiple Basalzellkarzinome im jüngeren Lebensalter mit dem Gorlin-Syndrom dar.